Juvenile xanthogranuloma - Xanthogranuloma Ngora
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ReferencesJuvenile xanthogranuloma (JXG) mangrupikeun kaayaan anu cukup umum sareng jinis non‑Langerhans cell histiocytic disorder anu paling sering di barudak. Dina sakitar 75 % kasus, lesi ieu muncul dina taun mimiti kahirupan, sareng langkung ti 15‑20 % pasien ngagaduhan éta ti lahir. Sanajan jarang di déwasa, JXG ilaharna lumangsung paling sering dina jalma di ahir duapuluhan nepi ka tilu puluhan, sarta mayoritas penderita sawawa boga ngan hiji lesi. Sacara klinis, éta némbongan salaku nabrak atanapi gumpalan konéng‑oranyeu‑coklat tunggal atawa sababaraha, utamina dina raray, beuheung, jeung awak luhur. Lesi dina lisan jarang, tapi bisa muncul salaku benjolan konéng dina sisi létah atawa di tempat séjén dina sungut, anu tiasa nyababkeun borok jeung perdarahan. Lesi kulit biasana teu ngabalukarkeun gejala sarta condong ngaleungit sorangan dina sababaraha taun. Sanajan jarang, involvement ocular mangrupakeun masalah paling umum saluareun kulit, dituturkeun ku involvement paru. Ocular JXG ilaharna mangaruhan ngan hiji panon sarta lumangsung dina kirang ti 0,5 % pasien, sanajan kira‑kira 40 % jalma kalayan involvement ocular ogé boga sababaraha lesi kulit nalika didiagnosis.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Juvenile xanthogranulomas (JXGs) mangrupakeun panyakit jinak anu jarang, bagian tina kategori non‑Langerhans cell histiocytoses anu langkung ageung. Aranjeunna ilaharna muncul salaku hiji atawa leuwih benjolan beureum atawa koneng, mindeng kapanggih dina sirah atawa beuheung. Kaseueuran JXGs muncul boh dina kalahiran atawa dina taun kahiji kahirupan. Sanajan jarang, sakapeung JXGs tiasa mangaruhan bagian awak séjén salian kulit, sarta keterlibatan panon kudu dipariksa nurutkeun literatur anu aya. Sacara umum, JXG dina kulit ngaleungit sorangan sareng biasana henteu peryogi perawatan.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Lesi ocular muncul dina nepi ka 10 % jalma anu ngalaman JXG sarta tiasa mangaruhan visi maranéhanana. Sanajan lesi kulit biasana ngaleungit sorangan, lesi okular jarang réngsé sorangan sareng mindeng peryogi perlakuan.